Ebstein Anomaly

Ebstein anomaly is a rare (~0.005% of the general population) congenital heart condition characterized by the apical displacement of the septal tricuspid valve (TV) leaflet, a “sail-like,” long anterior TV leaflet, atrialization of the proximal right ventricle (RV), and a dilated TV annulus. These anatomic changes result in tricuspid regurgitation and RV dysfunction.

Apical 5-chamber transthoracic echocardiogram view showing Ebstein anomaly.

Ebstein anomaly is associated with interatrial findings like patent foramen ovale and secundum atrial septal defect. Furthermore, conduction abnormalities via accessory pathways (Wolff-Parkinson-White syndrome) can precipitate arrhythmias.

Previous article
Next article

Related Articles


Please enter your comment!
Please enter your name here

Try EchoTools - my free, iOS ultrasonography reference application!

Latest Articles