Ebstein anomaly is a rare (~0.005% of the general population) congenital heart condition characterized by the apical displacement of the septal tricuspid valve (TV) leaflet, a “sail-like,” long anterior TV leaflet, atrialization of the proximal right ventricle (RV), and a dilated TV annulus. These anatomic changes result in tricuspid regurgitation and RV dysfunction.
Ebstein anomaly is associated with interatrial findings like patent foramen ovale and secundum atrial septal defect. Furthermore, conduction abnormalities via accessory pathways (Wolff-Parkinson-White syndrome) can precipitate arrhythmias.
